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VOLUME 10 , ISSUE 2 ( May-August, 2023 ) > List of Articles


A Rare Case of Optic Nerve Sheath Meningioma

Sivaroja Yellaturi, K Mugundhan, Sowmini Perumal, Sakthi Velayutham, Malcolm Jeyaraj, V Kannan, R Viveka Saravanan

Keywords : Meningiomas, Neurofibromatosis, Optic nerve sheath

Citation Information : Yellaturi S, Mugundhan K, Perumal S, Velayutham S, Jeyaraj M, Kannan V, Saravanan RV. A Rare Case of Optic Nerve Sheath Meningioma. Bengal Physician Journal 2023; 10 (2):55-58.

DOI: 10.5005/jp-journals-10070-8001

License: CC BY-NC 4.0

Published Online: 07-08-2023

Copyright Statement:  Copyright © 2023; The Author(s).


Optic nerve sheath meningiomas (ONSMs) are benign neoplasms originating from the arachnoid cap cells located in the dural sheath surrounding the orbital or intracanalicular portion of the optic nerve. Multiple meningiomas have most commonly been found to be associated with neurofibromatosis type 2 (NF2). Although optic nerve sheath meningiomas are benign and slow growing, they tend to cause severe vision loss at later stages. Patients with meningiomas at one site should be screened for meningiomas at other locations and also for the presence of neurocutaneous stigmata.

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