Uveitis and Retinal Vasculitis—Harbingers of Neuro-Behcet\'s Disease: A Case Report

Pramod Kumar Samala; Sowmini Perumal; Sakthi Velayudham; Malcolm Jeyaraj; Kannan Vellaichamy; Viveka Saravanan Raju; Mugundhan Krishnan

doi:10.5005/jp-journals-10070-8022

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Uveitis and Retinal Vasculitis—Harbingers of Neuro-Behcet's Disease: A Case Report

Pramod Kumar Samala, Sowmini Perumal, Sakthi Velayudham, Malcolm Jeyaraj, Kannan Vellaichamy, Viveka Saravanan Raju, Mugundhan Krishnan

Keywords : Case report, Neuro-Behcet's disease, Retinal vasculitis, Stroke-like episodes

Citation Information : Samala PK, Perumal S, Velayudham S, Jeyaraj M, Vellaichamy K, Raju VS, Krishnan M. Uveitis and Retinal Vasculitis—Harbingers of Neuro-Behcet's Disease: A Case Report. Bengal Physician Journal 2023; 10 (3):102-104.

DOI: 10.5005/jp-journals-10070-8022

License: CC BY-NC 4.0

Published Online: 21-12-2023

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Abstract

We report this case of Neuro-Behcet's disease who initially had recurrent episodes of uveitis over a period of 14 years and was under ophthalmological follow-up. Recently, she developed retinal vasculitis and multiple stroke-like episodes. She was evaluated for Behcet's disease. Pathergy test and HLAB51 were positive. She had characteristic diencephalic lesions on neuroimaging and responded well to immunotherapy. Key message: Uveitis and retinal vasculitis may be harbingers of Neuro-Behcet's disease. Rare neurological manifestations such as stroke-like episodes can occur much later in the course of Behcet's disease with unique neuroimaging findings.

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