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VOLUME 9 , ISSUE 2 ( May-August, 2022 ) > List of Articles

Case Of The Quarter

Left Ventricular Noncompaction Cardiomyopathy Managed with Cardiac Resynchronization Therapy: A Case Report

Mainak Mukhopadhyay, Pradipta Som, Rajkumar Mondal, Pinaki Maiti

Keywords : Cardiac resynchronization therapy, Cardiomyopathy, Conduction abnormality, Dyssynchrony, Heart failure with reduced ejection fraction, Left ventricular noncompaction

Citation Information : Mukhopadhyay M, Som P, Mondal R, Maiti P. Left Ventricular Noncompaction Cardiomyopathy Managed with Cardiac Resynchronization Therapy: A Case Report. Bengal Physician Journal 2022; 9 (2):35-40.

DOI: 10.5005/jp-journals-10070-7081

License: CC BY-NC 4.0

Published Online: 31-08-2022

Copyright Statement:  Copyright © 2022; The Author(s).


Although “spongy myocardium” was first observed by Grant in 1926, left ventricular noncompaction (LVNC) cardiomyopathy was originally described by Engberding and Bender in 1984.1 Left ventricular noncompaction cardiomyopathy is characterized by abnormal ventricular myocardial protrusions with a thin layer of properly compacted myocardium.2,3 It is a rare entity, with a prevalence less than 0.02%.4 We report a case of LVNC cardiomyopathy with dyssynchrony, which was successfully managed with cardiac resynchronization therapy (CRT).

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