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VOLUME 12 , ISSUE 1 ( January-March, 2025 ) > List of Articles

PICTORIAL ESSAY

Fibromuscular Dysplasia Presenting as Posterior Reversible Encephalopathy Syndrome in a Young Female

Souvik Das, Atanu Chandra

Keywords : Case report, Fibromuscular dysplasia, Hypertensive emergency, Posterior reversible encephalopathy syndrome, Renal artery stenosis, Renovascular hypertension

Citation Information : Das S, Chandra A. Fibromuscular Dysplasia Presenting as Posterior Reversible Encephalopathy Syndrome in a Young Female. Bengal Physician Journal 2025; 12 (1):52-53.

DOI: 10.5005/jp-journals-10070-8036

License: CC BY-NC 4.0

Published Online: 20-03-2025

Copyright Statement:  Copyright © 2025; The Author(s).


Abstract

Fibromuscular dysplasia (FMD) can present with renovascular hypertension with or without hypertensive emergency in mostly young patients. A 16-year-old girl presented with uncontrolled hypertension and features of posterior reversible encephalopathy syndrome (PRES). She had no features of large vessel vasculitis. Renal artery bruit could be auscultated on the right side. Blood examination showed hyperreninemic hyperaldosteronism. The USG renal artery doppler study and invasive renal angiogram showed unilateral right renal artery stenosis. She was provisionally diagnosed as a case of FMD and was treated accordingly.

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